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| Evidence for human transmission of amyloid-β pathology and cerebral amyloid angiopathy Z Jaunmuktane, S Mead, M Ellis, JDF Wadsworth, AJ Nicoll, J Kenny, ... Nature 525 (7568), 247-250, 2015 | 588 | 2015 |
| Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report SJ Wroe, S Pal, D Siddique, H Hyare, R Macfarlane, S Joiner, JM Linehan, ... The Lancet 368 (9552), 2061-2067, 2006 | 505 | 2006 |
| BSE prions propagate as either variant CJD‐like or sporadic CJD‐like prion strains in transgenic mice expressing human prion protein EA Asante, JM Linehan, M Desbruslais, S Joiner, I Gowland, AL Wood, ... The EMBO journal, 2002 | 457 | 2002 |
| Molecular classification of sporadic Creutzfeldt–Jakob disease AF Hill, S Joiner, JDF Wadsworth, KCL Sidle, JE Bell, H Budka, ... Brain 126 (6), 1333-1346, 2003 | 408 | 2003 |
| Strain-specific prion-protein conformation determined by metal ions JDF Wadsworth, AF Hill, S Joiner, GS Jackson, AR Clarke, J Collinge Nature cell biology 1 (1), 55-59, 1999 | 375 | 1999 |
| Human prion protein with valine 129 prevents expression of variant CJD phenotype JDF Wadsworth, EA Asante, M Desbruslais, JM Linehan, S Joiner, ... Science 306 (5702), 1793-1796, 2004 | 319 | 2004 |
| A naturally occurring variant of the human prion protein completely prevents prion disease EA Asante, M Smidak, A Grimshaw, R Houghton, A Tomlinson, A Jeelani, ... Nature 522 (7557), 478-481, 2015 | 207 | 2015 |
| Molecular and clinical classification of human prion disease JDF Wadsworth, AF Hill, JA Beck, J Collinge British medical bulletin 66 (1), 241-254, 2003 | 198 | 2003 |
| Disease-related prion protein forms aggresomes in neuronal cells leading to caspase activation and apoptosis M Kristiansen, MJ Messenger, PC Klohn, S Brandner, JDF Wadsworth, ... Journal of Biological Chemistry 280 (46), 38851-38861, 2005 | 186 | 2005 |
| Chronic wasting disease prions are not transmissible to transgenic mice overexpressing human prion protein MK Sandberg, H Al-Doujaily, CJ Sigurdson, M Glatzel, C O'Malley, ... Journal of General Virology 91 (10), 2651-2657, 2010 | 171 | 2010 |
| Detection and characterization of proteinase K-sensitive disease-related prion protein with thermolysin S Cronier, N Gros, MH Tattum, GS Jackson, AR Clarke, J Collinge, ... Biochemical Journal 416 (2), 297-305, 2008 | 168 | 2008 |
| Variant Creutzfeldt–Jakob Disease in a Patient with Heterozygosity at PRNP Codon 129 T Mok, Z Jaunmuktane, S Joiner, T Campbell, C Morgan, B Wakerley, ... New England Journal of Medicine 376 (3), 292-294, 2017 | 163 | 2017 |
| A novel prion disease associated with diarrhea and autonomic neuropathy S Mead, S Gandhi, J Beck, D Caine, D Gajulapalli, C Carswell, H Hyare, ... New England Journal of Medicine 369 (20), 1904-1914, 2013 | 163 | 2013 |
| Prion neuropathology follows the accumulation of alternate prion protein isoforms after infective titre has peaked MK Sandberg, H Al-Doujaily, B Sharps, MW De Oliveira, C Schmidt, ... Nature communications 5 (1), 4347, 2014 | 161 | 2014 |
| Phenotypic heterogeneity and genetic modification of P102L inherited prion disease in an international series TEF Webb, M Poulter, J Beck, J Uphill, G Adamson, T Campbell, ... Brain 131 (10), 2632-2646, 2008 | 153 | 2008 |
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| Update on human prion disease JDF Wadsworth, J Collinge Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1772 (6), 598-609, 2007 | 149 | 2007 |
| Amyloid-β nanotubes are associated with prion protein-dependent synaptotoxicity AJ Nicoll, S Panico, DB Freir, D Wright, C Terry, E Risse, CE Herron, ... Nature communications 4 (1), 2416, 2013 | 144 | 2013 |
| Inherited prion disease with six octapeptide repeat insertional mutation—molecular analysis of phenotypic heterogeneity S Mead, M Poulter, J Beck, TEF Webb, TA Campbell, JM Linehan, ... Brain 129 (9), 2297-2317, 2006 | 139 | 2006 |
