Mice transgenic for the human myotonic dystrophy region with expanded CTG repeats display muscular and brain abnormalities H Seznec, O Agbulut, N Sergeant, C Savouret, A Ghestem, N Tabti, ... Human Molecular Genetics 10 (23), 2717-2726, 2001 | 275 | 2001 |
Friedreich ataxia: the oxidative stress paradox H Seznec, D Simon, C Bouton, L Reutenauer, A Hertzog, P Golik, ... Human molecular genetics 14 (4), 463-474, 2005 | 245 | 2005 |
Friedreich ataxia mouse models with progressive cerebellar and sensory ataxia reveal autophagic neurodegeneration in dorsal root ganglia D Simon, H Seznec, A Gansmuller, N Carelle, P Weber, D Metzger, ... Journal of Neuroscience 24 (8), 1987-1995, 2004 | 227 | 2004 |
Transgenic mice carrying large human genomic sequences with expanded CTG repeat mimic closely the DM CTG repeat intergenerational and somatic instability H Seznec, AS Lia-Baldini, C Duros, C Fouquet, C Lacroix, ... Human molecular genetics 9 (8), 1185-1194, 2000 | 211 | 2000 |
Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia H Seznec, D Simon, L Monassier, P Criqui-Filipe, A Gansmuller, P Rustin, ... Human molecular genetics 13 (10), 1017-1024, 2004 | 162 | 2004 |
Modeling radiation chemistry in the Geant4 toolkit M Karamitros, A Mantero, S Incerti, W Friedland, G Baldacchino, ... Prog Nucl Sci Technol 2 (0), 2011 | 131 | 2011 |
Somatic instability of the CTG repeat in mice transgenic for the myotonic dystrophy region is age dependent but not correlated to the relative intertissue transcription levels … AS Lia, H Seznec, H Hofmann-Radvanyi, F Radvanyi, C Duros, C Saquet, ... Human molecular genetics 7 (8), 1285-1291, 1998 | 106 | 1998 |
Cobalt distribution in keratinocyte cells indicates nuclear and perinuclear accumulation and interaction with magnesium and zinc homeostasis R Ortega, C Bresson, A Fraysse, C Sandre, G Devès, C Gombert, ... Toxicology letters 188 (1), 26-32, 2009 | 97 | 2009 |
Functionalized nanomaterials: their use as contrast agents in bioimaging: mono-and multimodal approaches Q Le Trequesser, H Seznec, MH Delville Nanotechnology Reviews 2 (2), 125-169, 2013 | 81 | 2013 |
Monte Carlo dosimetry for targeted irradiation of individual cells using a microbeam facility S Incerti, H Seznec, M Simon, P Barberet, C Habchi, P Moretto Radiation protection dosimetry 133 (1), 2-11, 2009 | 77 | 2009 |
Live cell imaging of mitochondria following targeted irradiation in situ reveals rapid and highly localized loss of membrane potential DWM Walsh, C Siebenwirth, C Greubel, K Ilicic, J Reindl, S Girst, ... Scientific Reports 7 (1), 46684, 2017 | 64 | 2017 |
Titanium dioxide nanoparticles induced intracellular calcium homeostasis modification in primary human keratinocytes. Towards an in vitro explanation of titanium dioxide … M Simon, P Barberet, MH Delville, P Moretto, H Seznec Nanotoxicology 5 (2), 125-139, 2011 | 60 | 2011 |
Monte-Carlo dosimetry on a realistic cell monolayer geometry exposed to alpha particles P Barberet, F Vianna, M Karamitros, T Brun, N Gordillo, P Moretto, ... Physics in Medicine & Biology 57 (8), 2189, 2012 | 49 | 2012 |
In situ quantification of diverse titanium dioxide nanoparticles unveils selective endoplasmic reticulum stress-dependent toxicity M Simon, G Saez, G Muggiolu, M Lavenas, Q Le Trequesser, C Michelet, ... Nanotoxicology 11 (1), 134-145, 2017 | 48 | 2017 |
First results obtained using the CENBG nanobeam line: performances and applications P Barberet, L Daudin, N Gordillo, S Sorieul, M Simon, H Seznec, ... Nuclear Instruments and Methods in Physics Research Section B: Beam …, 2011 | 39 | 2011 |
Monte Carlo simulation of the CENBG microbeam and nanobeam lines with the Geant4 toolkit S Incerti, Q Zhang, F Andersson, P Moretto, GW Grime, MJ Merchant, ... Nuclear Instruments and Methods in Physics Research Section B: Beam …, 2007 | 38 | 2007 |
Fluorescence time-lapse imaging of single cells targeted with a focused scanning charged-particle microbeam S Bourret, F Vianna, G Devès, V Atallah, P Moretto, H Seznec, P Barberet Nuclear Instruments and Methods in Physics Research Section B: Beam …, 2014 | 34 | 2014 |
Single Cell In Situ Detection and Quantification of Metal Oxide Nanoparticles Using Multimodal Correlative Microscopy Q Le Trequesser, G Devès, G Saez, L Daudin, P Barberet, C Michelet, ... Analytical chemistry 86 (15), 7311-7319, 2014 | 32 | 2014 |
Advances in microbeam technologies and applications to radiation biology P Barberet, H Seznec Radiation protection dosimetry 166 (1-4), 182-187, 2015 | 30 | 2015 |
Modeling proton and alpha elastic scattering in liquid water in Geant4-DNA HN Tran, Z El Bitar, C Champion, M Karamitros, MA Bernal, Z Francis, ... Nuclear Instruments and Methods in Physics Research Section B: Beam …, 2015 | 30 | 2015 |