| IL-22 mediates mucosal host defense against Gram-negative bacterial pneumonia SJ Aujla, YR Chan, M Zheng, M Fei, DJ Askew, DA Pociask, TA Reinhart, ... Nature medicine 14 (3), 275-281, 2008 | 1523 | 2008 |
| Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation FJ Accurso, SM Rowe, JP Clancy, MP Boyle, JM Dunitz, PR Durie, ... New England Journal of Medicine 363 (21), 1991-2003, 2010 | 941 | 2010 |
| Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation JP Clancy, SM Rowe, FJ Accurso, ML Aitken, RS Amin, MA Ashlock, ... Thorax 67 (1), 12-18, 2012 | 662 | 2012 |
| Role of CFTR in airway disease JM Pilewski, RA Frizzell Physiological reviews 79 (1), S215-S255, 1999 | 626 | 1999 |
| Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-α and granulocyte colony-stimulating factor in bronchial epithelium: implications for … F McAllister, A Henry, JL Kreindler, PJ Dubin, L Ulrich, C Steele, ... The Journal of Immunology 175 (1), 404-412, 2005 | 538 | 2005 |
| Egr-1 regulates autophagy in cigarette smoke-induced chronic obstructive pulmonary disease ZH Chen, HP Kim, FC Sciurba, SJ Lee, C Feghali-Bostwick, DB Stolz, ... PloS one 3 (10), e3316, 2008 | 531 | 2008 |
| High IFN-γ and low SLPI mark severe asthma in mice and humans M Raundhal, C Morse, A Khare, TB Oriss, J Milosevic, J Trudeau, R Huff, ... The Journal of clinical investigation 125 (8), 3037-3050, 2015 | 405 | 2015 |
| Comprehensive gene expression profiles reveal pathways related to the pathogenesis of chronic obstructive pulmonary disease W Ning, CJ Li, N Kaminski, CA Feghali-Bostwick, SM Alber, YP Di, ... Proceedings of the National Academy of Sciences 101 (41), 14895-14900, 2004 | 400 | 2004 |
| Autoantibodies in patients with chronic obstructive pulmonary disease CA Feghali-Bostwick, AS Gadgil, LE Otterbein, JM Pilewski, MW Stoner, ... American journal of respiratory and critical care medicine 177 (2), 156-163, 2008 | 395 | 2008 |
| Epithelial Na+ channels are fully activated by furin-and prostasin-dependent release of an inhibitory peptide from the γ-subunit JB Bruns, MD Carattino, S Sheng, AB Maarouf, OA Weisz, JM Pilewski, ... Journal of Biological Chemistry 282 (9), 6153-6160, 2007 | 359 | 2007 |
| Repeated aerosolized AAV-CFTR for treatment of cystic fibrosis: a randomized placebo-controlled phase 2B trial RB Moss, C Milla, J Colombo, F Accurso, PL Zeitlin, JP Clancy, ... Human gene therapy 18 (8), 726-732, 2007 | 325 | 2007 |
| T lymphocytes adhere to airway smooth muscle cells via integrins and CD44 and induce smooth muscle cell DNA synthesis. AL Lazaar, SM Albelda, JM Pilewski, B Brennan, E Puré, RA Panettieri Jr The Journal of experimental medicine 180 (3), 807-816, 1994 | 308 | 1994 |
| Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis DM Hutt, D Herman, APC Rodrigues, S Noel, JM Pilewski, J Matteson, ... Nature chemical biology 6 (1), 25-33, 2010 | 288 | 2010 |
| Insulin-like growth factor binding proteins 3 and 5 are overexpressed in idiopathic pulmonary fibrosis and contribute to extracellular matrix deposition JM Pilewski, L Liu, AC Henry, AV Knauer, CA Feghali-Bostwick The American journal of pathology 166 (2), 399-407, 2005 | 274 | 2005 |
| Insulin therapy to improve BMI in cystic fibrosis–related diabetes without fasting hyperglycemia: results of the Cystic Fibrosis Related Diabetes Therapy Trial A Moran, P Pekow, P Grover, M Zorn, B Slovis, J Pilewski, E Tullis, ... Diabetes care 32 (10), 1783-1788, 2009 | 262 | 2009 |
| Lung tissues in patients with systemic sclerosis have gene expression patterns unique to pulmonary fibrosis and pulmonary hypertension E Hsu, H Shi, RM Jordan, J Lyons‐Weiler, JM Pilewski, ... Arthritis & Rheumatism 63 (3), 783-794, 2011 | 243 | 2011 |
| Voriconazole prophylaxis in lung transplant recipients S Husain, DL Paterson, S Studer, J Pilewski, M Crespo, D Zaldonis, ... American Journal of Transplantation 6 (12), 3008-3016, 2006 | 243 | 2006 |
| Efficacy of extracorporeal membrane oxygenation as a bridge to lung transplantation Y Toyoda, JK Bhama, N Shigemura, D Zaldonis, J Pilewski, M Crespo, ... The Journal of thoracic and cardiovascular surgery 145 (4), 1065-1071, 2013 | 240 | 2013 |
| Patients with idiopathic pulmonary fibrosis with antibodies to heat shock protein 70 have poor prognoses RA Kahloon, J Xue, A Bhargava, E Csizmadia, L Otterbein, DJ Kass, ... American journal of respiratory and critical care medicine 187 (7), 768-775, 2013 | 220 | 2013 |
| Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR SH Donaldson, JM Pilewski, M Griese, J Cooke, L Viswanathan, E Tullis, ... American journal of respiratory and critical care medicine 197 (2), 214-224, 2018 | 218 | 2018 |
